Isolated Juvenile Xanthogranuloma in Thoracic Spine: Intraoperative Cytological Diagnosis of a Rare Presentation

Juvenile Xanthogranuloma (JXG) is a benign proliferative disorder of non-Langerhans histiocytes, occurring in vast majority of cases as multiple, selflimited, cutaneous lesions of children in the first two decades of life [1]. Extracutaneous manifestations of JXG are uncommon, and isolated JXG involving the spinal column is extremely rare [2]. We hereby report the clinicopathological features of a 9 month old boy and characterize a case of isolated JXG in the thoracic spine. This case report draws attention to the fact that isolated xanthogranuloma of the central nervous system should be considered among possible diagnosis of subdural extramedullary spinal masses in children and young adults.